Rapidly growing primitive neuroectodermal tumor of the uterus causing obstructive uropathy in a 13-year-old African girl: A case report
DOI:
https://doi.org/10.59692/jogeca.v37i3.28Keywords:
embryonal tumors, obstructive uropathy, primitive neuroectodermal tumor, uterusAbstract
Background: Uterine primitive neuroectodermal tumors (PNETs) are a rare group of embryonal tumors, with less than 100 cases reported, mostly in postmenopausal women. Their rarity poses diagnostic and management challenges, contributing to high mortality.
Case presentation: A 13-year-old presented with a 2-month history of abdominal pain, swelling, and heavy menstruation. Physical examination revealed a firm, fixed, nontender pelvic mass. She underwent a panhysterectomy and nodal resection. Histopathology confirmed PNET. The tumor recurred within a month, and intraoperative spillage occurred during repeat surgery. She developed obstructive uropathy and succumbed approximately 11 months after initial presentation.
Conclusion: Uterine PNETs are aggressive tumors that rapidly infiltrate and obstruct pelvic structures. Owing to their rarity, diagnosis and management remain challenging, with high mortality.
Keywords: embryonal tumors, obstructive uropathy, primitive neuroectodermal tumor, uterus
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Copyright (c) 2025 JOEL OOKO OJWANDO, Dr. Mokomba, Pro. Cheresem, Dr. Walong
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